Variables | Categories | Adjusted HR (95% CI) | Points |
Age yrs | ≥70 | 2.20 (1.35–3.61) | 1 |
<70 (reference) | 0 | ||
Sex | Male | 2.01 (1.15–3.51) | 1 |
Female (reference) | 0 | ||
Aetiology | CTD-PAH-SSc or Group I PAH others# | 2.33 (1.42–3.82) | 1 |
Idiopathic, heritable, anorexigen-associated PAH or CTD-PAH non-SSc | 0 | ||
6MWD m | <50 | 5.04 (2.33–10.89) | 3 |
50–149 | 3.45 (1.48–8.05) | 2 | |
150–299 | 2.48 (1.28–4.79) | 1 | |
≥300 (reference) | 0 | ||
Pra mmHg | ≥10 | 1.50 (0.90–2.49) | 1 |
<10 (reference) | 0 | ||
CO L·min−1 | <3 | 2.18 (1.32–3.61) | 1 |
≥3 (reference) | 0 |
6MWD: 6-min walk distance; Pra: right atrial pressure; CO: cardiac output; CTD-PAH: connective tissue disease associated pulmonary arterial hypertension (PAH); SSc: systemic sclerosis; #: includes portopulmonary hypertension, HIV and pulmonary veno-occlusive disease.