PT  - JOURNAL ARTICLE
AU  - Banque, Maria Niña
TI  - Congenital pulmonary airway malformation in a 10 year old male adolescent
DP  - 2011 Sep 01
TA  - European Respiratory Journal
PG  - p2433
VI  - 38
IP  - Suppl 55
4099  - https://publications.ersnet.org//content/38/Suppl_55/p2433.short
4100  - https://publications.ersnet.org//content/38/Suppl_55/p2433.full
SO  - Eur Respir J2011 Sep 01; 38
AB  - Congenital pulmonary airway malformation (CPAM), more commonly and previously termed congenital cystic adenomatoid malformation is an uncommon anomaly characterized by multicystic lesions due to proliferation of the respiratory bronchioles. This lung anomaly has an incidence of 1:25,000-35,000 and 90% of this number occurs in children below 2 years old. Late-onset CPAM is an infrequent illness and requires a high level of suspicion. It usually presents in the form of repeated infections but very rarely remains to be asymptomatic until its diagnosis. This is a case of a previously healthy, apparently asymptomatic 10 year old male adolescent who had an incidental finding of a pulmonary bulla on chest radiograph taken while he was worked up because of a high grade fever which eventually he was diagnosed of dengue fever. He underwent elective right upper lobe lobectomy and was discharged improved on the 4th post-operative day. The final histopathologic result is consistent with a congenital pulmonary airway malformation, type 1.