PT  - JOURNAL ARTICLE
AU  - V Thomas de Montpreville
AU  - E Dulmet
AU  - R Ponlot
AU  - P Dartevelle
TI  - Giant bilateral fibrous dysplasia of first ribs: compression of mediastinum and thoracic outlet
AID  - 10.1183/09031936.95.08061028
DP  - 1995 Jun 01
TA  - European Respiratory Journal
PG  - 1028--1029
VI  - 8
IP  - 6
4099  - http://erj.ersjournals.com/content/8/6/1028.short
4100  - http://erj.ersjournals.com/content/8/6/1028.full
SO  - Eur Respir J1995 Jun 01; 8
AB  - A 43 year old woman presented with two large bilateral tumours of the first ribs that compressed the right subclavian vessels, trachea and oesophagus and led to right arm oedema, severe dyspnoea and dysphagia. The resected tumours showed typical histological features of fibrous dysplasia without malignant transformation. The right tumour weighed 1.5 kg and measured 17 x 13 x 10 cm. This report demonstrates that major surgery is still possible for resection of such exceptional giant compressive lesions, since fibrous dysplasia is a benign and non-infiltrative tumour.