RT Journal Article
SR Electronic
T1 Sole pulmonary involvement by Langerhans' cell histiocytosis in a child
JF European Respiratory Journal
JO Eur Respir J
FD European Respiratory Society
SP 1226
OP 1228
DO 10.1183/09031936.93.06081226
VO 6
IS 8
A1 JM Chatkin
A1 JC Bastos
A1 RT Stein
A1 AM Gaiger
YR 1993
UL http://erj.ersjournals.com/content/6/8/1226.abstract
AB The case of a boy aged 4 yrs and 7 months, with isolated pulmonary involvement by Langerhans' cell histiocytosis is reported. The presentation of the disease was a sudden pneumothorax, with no previous signs of respiratory disease. The case was confirmed by S-100 and MT1 antibody staining, and was treated with pulse steroids and several pleural drainages, until the boy died after a large bilateral pneumothorax.