PT  - JOURNAL ARTICLE
AU  - L Tabak
AU  - D Yilmazbayhan
AU  - Z Kilicaslan
AU  - C Tascioglu
AU  - M Agan
TI  - Value of bronchoalveolar lavage in lipidoses with pulmonary involvement
AID  - 10.1183/09031936.94.07020409
DP  - 1994 Feb 01
TA  - European Respiratory Journal
PG  - 409--411
VI  - 7
IP  - 2
4099  - http://erj.ersjournals.com/content/7/2/409.short
4100  - http://erj.ersjournals.com/content/7/2/409.full
SO  - Eur Respir J1994 Feb 01; 7
AB  - Adult lipid storage disorders with pulmonary involvement are rare and usually diagnosed at autopsy. We report a patient with splenomegaly and reticulonodular pattern on lung computed tomography. Bronchoalveolar lavage was performed and revealed the presence of lipid-containing foamy cells, with the demonstration of both periodic acid-Schiff (PAS) and scharlach red stain positive vacuoles in the cytoplasm of alveolar macrophages. The same cells were found in bone marrow biopsy. As in other rare disorders, bronchoalveolar lavage may be of diagnostic value in lipid storage disorders with pulmonary involvement.