PT  - JOURNAL ARTICLE
AU  - E Azoulay
AU  - B Paugam
AU  - MF Heymann
AU  - M Kambouchner
AU  - A Haloun
AU  - D Valeyre
AU  - JP Battesti
AU  - A Tazi
TI  - Familial extensive idiopathic bilateral pleural fibrosis
AID  - 10.1034/j.1399-3003.1999.14d41.x
DP  - 1999 Oct 01
TA  - European Respiratory Journal
PG  - 971--973
VI  - 14
IP  - 4
4099  - http://erj.ersjournals.com/content/14/4/971.short
4100  - http://erj.ersjournals.com/content/14/4/971.full
SO  - Eur Respir J1999 Oct 01; 14
AB  - The authors report three sisters with bilateral isolated apical pleural fibrosis of unknown origin, which did not respond to empirical antituberculosis therapy and oral corticosteroids. The disease evolved in an unrelenting fashion producing pleural fibrosis at the lung bases and leading to the death of two sisters and to lung transplantation in the other one. There was no history of other familial disease or consanguinity. The particular features of these cases and the differences from other reports of apparently cryptogenic pleural fibrosis are outlined.