PT - JOURNAL ARTICLE AU - Hekelaar, N AU - van Uffelen, R AU - van Vliet, AC AU - Varin, OC AU - Westenend, PJ TI - Primary lymphoepithelioma-like carcinoma within an intralobular pulmonary sequestration AID - 10.1183/09031936.00.16510250 DP - 2000 Nov 01 TA - European Respiratory Journal PG - 1025--1027 VI - 16 IP - 5 4099 - https://publications.ersnet.org//content/16/5/1025.short 4100 - https://publications.ersnet.org//content/16/5/1025.full SO - Eur Respir J2000 Nov 01; 16 AB - A 31-yr-old Chinese female, a nonsmoker, presented with digital clubbing and coughing. Diagnostic evaluation revealed a pulmonary sequestration in the left lower lobe. During surgery a tumour was discovered, which turned out to be a lymphoepithelioma-like carcinoma. These tumours are mainly found in Asians, and are associated with the Epstein Barr virus and not with smoking. They are thought to have a better prognosis and to be more chemosensitive. The need for surgical treatment of pulmonary sequestration and the recognition of lymphoepithelioma-like carcinoma as a distinct clinicopathological entity is emphasized.