TY - JOUR T1 - The features of rare pulmonary tumors and their surgical treatment JF - European Respiratory Journal JO - Eur Respir J DO - 10.1183/13993003.congress-2020.1707 VL - 56 IS - suppl 64 SP - 1707 AU - Vadim Pischik AU - Evgenii Zinchenko AU - Aleksander Kovalenko AU - Olga Maslak Y1 - 2020/09/07 UR - http://erj.ersjournals.com/content/56/suppl_64/1707.abstract N2 - Rare pulmonary tumors (RPT) pose challenges for diagnosis, treatments and clinical decision making. Information about them is scant. Aim. To supplement information on diagnosis and surgical treatment of the RPT. Methods. A retrospective study of 499 lung resections for primary tumors, performed in St. Petersburg Federal hospital 122 in 2010-2019 was done. Every specimen has been investigated by immunostaining. Selection criteria for RPT: the RARECARE project principles (the incidence less than 6/100000 new cases per year), WHO Classification of Lung Tumors (2015). Results. After morphological investigation, 89/499 (17.84%) patients with RPT were diagnosed. There were 45 male, 44 female; mean age 54.02±14.7 years. According to ICD-O classification 74 tumors (83.1%) were malignant (/3); 9 (10.1%) – uncertain (/1); 6 (6.8%) tumors were benign (/0). Epithelial tumors comprise 79.8% (71 cases) with domination of atypical carcinoid (33); 15 tumors were mesenchymal (16.8%) with 6 myofibroblastic and 3 – primary pulmonary lymphomas. A correct preoperative diagnosis received in 22 (24.7%) patients. 66 (85.4%) patients underwent anatomical pulmonary resections, and the rest wedge resections performed for carcinoid tumors and low grade sarcomas. 77 (86.5%) procedures was done by VATS. All resections were R0. A frozen section was incorrect as well in 4 out of 7 cases, which required staged reVATS to expand the volume of surgery in 1 case. Conclusion. The study demonstrates a high incidence of RPT and complexity of its preoperative diagnosis. VATS resection is a good diagnostic and treatment method, especially then R0 resection is reached. For ICD-O /3 RPT the anatomical pulmonary resection with lymphadenectomy is recommended.FootnotesCite this article as: European Respiratory Journal 2020; 56: Suppl. 64, 1707.This abstract was presented at the 2020 ERS International Congress, in session “Respiratory viruses in the "pre COVID-19" era”.This is an ERS International Congress abstract. No full-text version is available. Further material to accompany this abstract may be available at www.ers-education.org (ERS member access only). ER -