RT Journal Article
SR Electronic
T1 Multidisciplinary team meetings dedicated to children interstitial lung diseases (chILD) – a 2-years experience
JF European Respiratory Journal
JO Eur Respir J
FD European Respiratory Society
SP 5292
DO 10.1183/13993003.congress-2020.5292
VO 56
IS suppl 64
A1 Nadia Nathan
A1 Alice Hadchouel
A1 Maryem Sari Hassoun
A1 Céline Lustremant
A1 Delphine Habouria
A1 Annick Clement
A1 Ralph Epaud
A1 . For The Respirare And Respifil Groups
YR 2020
UL http://erj.ersjournals.com/content/56/suppl_64/5292.abstract
AB Introduction: ChILD represent a heterogeneous group of rare and mostly severe disorders. In France, around 400 patients with chILD are listed. In adults, multidisciplinary teams (MDT) meetings are recognized as a crucial tool in such rare lung diseases. We aim at reporting the French experience of MDT meetings for chILD.Methods: On-line, video-conference MDT meetings have been held every month since 2018. For each patient, a standardized form is filled up by the clinician and sent to the Reference center for rare lung diseases (www.respiFIL.fr, www.respirare.fr). The MDT meetings include experts in the field with the aim of discussing diagnosis or treatment issues related to ChILD. After the MDT meeting, a report is established and sent to the requesting team.Results: In the last 20 months, 20 MDT were held and 107 patients were discussed. Participants were pediatric pulmonologists, geneticists, genetic counselor, pathologist, pediatric radiologists, and adult pulmonologists. The median age of the patients was 2 years-old. They were mainly followed in France but 14 (13%) patients were presented by international colleagues. The demands included a diagnosis issue (2%), management (19%), or both (75%). The MDT meetings allowed to precise or modify the ILD etiology in 1/3 of the patients; and to excluded ILD in 11 (10%). ILD remained of undefined cause for 19 (24%) vs 25 (32%).Conclusion: MDT meetings for chILD are easily feasible. They provide an important epidemiologic input by increasing the chILD case collection (+25%). They are an opportunity to collectively improve our knowledge on diagnosis and management of these rare diseases and to discuss genetic council issues.FootnotesCite this article as: European Respiratory Journal 2020; 56: Suppl. 64, 5292.This abstract was presented at the 2020 ERS International Congress, in session “Respiratory viruses in the "pre COVID-19" era”.This is an ERS International Congress abstract. No full-text version is available. Further material to accompany this abstract may be available at www.ers-education.org (ERS member access only).