RT Journal Article
SR Electronic
T1 Report of the European Respiratory Society/European Cystic Fibrosis Society task force on the care of adults with cystic fibrosis
JF European Respiratory Journal
JO Eur Respir J
FD European Respiratory Society
SP 420
OP 428
DO 10.1183/13993003.00592-2015
VO 47
IS 2
A1 Elborn, J. Stuart
A1 Bell, Scott C.
A1 Madge, Susan L.
A1 Burgel, Pierre-Regis
A1 Castellani, Carlo
A1 Conway, Steven
A1 De Rijcke, Karleen
A1 Dembski, Birgit
A1 Drevinek, Pavel
A1 Heijerman, Harry G.M.
A1 Innes, J. Alistair
A1 Lindblad, Anders
A1 Marshall, Bruce
A1 Olesen, Hanne V.
A1 Reimann, Andreas L.
A1 Solé, Ampara
A1 Viviani, Laura
A1 Wagner, Thomas O.F.
A1 Welte, Tobias
A1 Blasi, Francesco
YR 2016
UL http://erj.ersjournals.com/content/47/2/420.abstract
AB The improved survival in people with cystic fibrosis has led to an increasing number of patients reaching adulthood. This trend is likely to be maintained over the next decades, suggesting a need to increase the number of centres with expertise in the management of adult patients with cystic fibrosis. These centres should be capable of delivering multidisciplinary care addressing the complexity of the disease, in addition to addressing the psychological burden on patients and their families. Further issues that require attention are organ transplantation and end of life management.Lung disease in adults with cystic fibrosis drives most of the clinical care requirements, and major life-threatening complications, such as respiratory infection, respiratory failure, pneumothorax and haemoptysis, and the management of lung transplantation require expertise from trained respiratory physicians. The taskforce therefore strongly reccommends that medical leadership in multidisciplinary adult teams should be attributed to a respiratory physician adequately trained in cystic fibrosis management.The task force suggests the implementation of a core curriculum for trainees in adult respiratory medicine and the selection and accreditation of training centres that deliver postgraduate training to the standards of the HERMES programme.Respiratory physicians, trained in adult CF management, should lead multidisciplinary teams taking care of patients http://ow.ly/SgRgj