Risk of acute arterial and venous thromboembolic events in eosinophilic granulomatosis with polyangiitis (Churg–Strauss syndrome)
Alessandra Bettiol, Renato Alberto Sinico, Franco Schiavon, Sara Monti, Enrica Paola Bozzolo, Franco Franceschini, Marcello Govoni, Claudio Lunardi, Giuseppe Guida, Giuseppe Lopalco, Giuseppe Paolazzi, Angelo Vacca, Gina Gregorini, Pietro Leccese, Matteo Piga, Fabrizio Conti, Paolo Fraticelli, Luca Quartuccio, Federico Alberici, Carlo Salvarani, Silvano Bettio, Simone Negrini, Carlo Selmi, Savino Sciascia, Gabriella Moroni, Loredana Colla, Carlo Manno, Maria Letizia Urban, Alfredo Vannacci, Maria Rosa Pozzi, Paolo Fabbrini, Stefano Polti, Mara Felicetti, Maria Rita Marchi, Roberto Padoan, Paolo Delvino, Roberto Caporali, Carlomaurizio Montecucco, Lorenzo Dagna, Adriana Cariddi, Paola Toniati, Silvia Tamanini, Federica Furini, Alessandra Bortoluzzi, Elisa Tinazzi, Lorenzo Delfino, Iuliana Badiu, Giovanni Rolla, Vincenzo Venerito, Florenzo Iannone, Alvise Berti, Roberto Bortolotti, Vito Racanelli, Guido Jeannin, Angela Padula, Alberto Cauli, Roberta Priori, Armando Gabrielli, Milena Bond, Martina Tedesco, Giulia Pazzola, Paola Tomietto, Marco Pellecchio, Chiara Marvisi, Federica Maritati, Alessandra Palmisano, Christian Dejaco, Johann Willeit, Stefan Kiechl, Iacopo Olivotto, Peter Willeit, Domenico Prisco, Augusto Vaglio, Giacomo Emmi on behalf of the Italian EGPA Consortium
European Respiratory Journal 2021 57: 2004158; DOI: 10.1183/13993003.04158-2020
Alessandra Bettiol
1Dept of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy
2Dept of Neurosciences, Psychology, Drug Research and Child Health (NEUROFARBA), University of Firenze, Firenze, Italy
Renato Alberto Sinico
3Dept of Medicine and Surgery, University of Milano – Bicocca and Nephrology Unit, ASST-Monza, Milan/Monza, Italy
Franco Schiavon
4Operative Unit of Rheumatology, Dept of Medicine DIMED, University Hospital of Padova, Padova, Italy
Sara Monti
5Division of Rheumatology, IRCCS Policlinico S.Matteo Foundation and University of Pavia, Pavia, Italy
6University of Pavia, Pavia, Italy
Enrica Paola Bozzolo
7Unit of Immunology, Rheumatology, Allergy and Rare Diseases (UnIRAR), IRCCS-San Raffaele Scientific Institute, Milan, Italy
Franco Franceschini
8Unit of Rheumatology and Clinical Immunology, University and ASST Spedali Civili, Brescia, Italy
Marcello Govoni
9Dept of Medical Sciences, University of Ferrara, Ferrara, Italy
10Rheumatology Unit, Azienda Ospedaliero-Universitaria S. Anna, Ferrara, Italy
Claudio Lunardi
11Dept of Medicine, University of Verona, Verona, Italy
Giuseppe Guida
12Allergy and Pneumology Unit, A.O.S. Croce e Carle, Cuneo, Italy
Giuseppe Lopalco
13Rheumatology Unit, Dept of Emergency and Organ Transplantation (DETO), Polyclinic Hospital, University of Bari, Bari, Italy
Giuseppe Paolazzi
14Dept of Rheumatology, Santa Chiara Hospital, Trento, Italy
Angelo Vacca
15Dept of Biomedical Sciences and Human Oncology, Unit of Internal Medicine “Guido Baccelli”, University of Bari “Aldo Moro” Medical School, Bari, Italy
Gina Gregorini
16Nephrology Unit, ASST Spedali Civili, Brescia, Italy
Pietro Leccese
17Rheumatology Dept of Lucania, San Carlo Hospital, Potenza, Italy
Matteo Piga
18Rheumatology, Dept of Medical Sciences and Public Health, University Clinic, Cagliari, Italy
Fabrizio Conti
19Rheumatology Unit, Dept of Clinical Internal, Anesthesiological and Cardiovascular Sciences, Sapienza University of Rome, Rome, Italy
Paolo Fraticelli
20Dept of Internal Medicine, Clinica Medica, Ospedali Riuniti, Ancona, Italy
Luca Quartuccio
21Rheumatology Clinic, Dept of Medicine (DAME), University of Udine, Udine, Italy
Federico Alberici
22Dept of Medical and Surgical Specialties, Radiological Sciences and Public Health, University of Brescia, Brescia, Italy
23Nephrology Unit, Spedali Civili Hospital, Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia, Brescia, Italy
Carlo Salvarani
24Azienda USL-IRCCS di Reggio Emilia and University of Modena and Reggio Emilia, Reggio Emilia, Italy
Silvano Bettio
25Rheumatology Unit, Internal Medicine Dept, Cattinara Teaching Hospital (ASUITS), Trieste, Italy
Simone Negrini
26Internal Medicine, Clinical Immunology and Translational Medicine Unit, IRCCS Ospedale Policlinico San Martino, Genoa, Italy
27Centre of Excellence for Biomedical Research and Dept of Internal Medicine, University of Genoa, Genoa, Italy
Carlo Selmi
28Division of Rheumatology and Clinical Immunology, Humanitas Clinical and Research Center IRCCS, Rozzano - Milan, Italy
29Dept of Biomedical Sciences, Humanitas University, Pieve Emanuele - Milan, Italy
Savino Sciascia
30Center of Research of Immunopathology and Rare Diseases – Coordinating Center of the Network for Rare Diseases of Piedmont and Aosta Valley, Dept of Clinical and Biological Sciences, University of Turin, Turin, Italy
31SCU Nephrology and Dialysis, S. Giovanni Bosco Hospital, Dept of Clinical and Biological Sciences, University of Turin, Turin, Italy
Gabriella Moroni
32Nephrology Unit, Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Milan, Italy
Loredana Colla
33Nephrology, Dialysis and Renal Transplant Division, Dept of Medical Sciences, “Città della Salute e della Scienza di Torino” University Hospital, University of Turin, Turin, Italy
Carlo Manno
34Dept of Emergency and Organ Transplantation, Nephrology, Dialysis and Transplant Unit, University of Bari “Aldo Moro”, Bari, Italy
Maria Letizia Urban
1Dept of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy
Alfredo Vannacci
2Dept of Neurosciences, Psychology, Drug Research and Child Health (NEUROFARBA), University of Firenze, Firenze, Italy
Maria Rosa Pozzi
3Dept of Medicine and Surgery, University of Milano – Bicocca and Nephrology Unit, ASST-Monza, Milan/Monza, Italy
Paolo Fabbrini
35Nephrology Unit, Hospital San Gerardo Monza, University of Milano Bicocca, Milan, Italy
Stefano Polti
3Dept of Medicine and Surgery, University of Milano – Bicocca and Nephrology Unit, ASST-Monza, Milan/Monza, Italy
Mara Felicetti
4Operative Unit of Rheumatology, Dept of Medicine DIMED, University Hospital of Padova, Padova, Italy
Maria Rita Marchi
36Respiratory Pathophysiology Division, University Hospital of Padova, Padova, Italy
Roberto Padoan
4Operative Unit of Rheumatology, Dept of Medicine DIMED, University Hospital of Padova, Padova, Italy
Paolo Delvino
5Division of Rheumatology, IRCCS Policlinico S.Matteo Foundation and University of Pavia, Pavia, Italy
6University of Pavia, Pavia, Italy
Roberto Caporali
37Division of Clinical Rheumatology, ASST Gaetano Pini-CTO Institute, Milan, Italy
38Dept of Clinical Sciences and Community Health, Research Center for Adult and Pediatric Rheumatic Diseases, Università degli Studi di Milano, Milan, Italy
Carlomaurizio Montecucco
5Division of Rheumatology, IRCCS Policlinico S.Matteo Foundation and University of Pavia, Pavia, Italy
Lorenzo Dagna
7Unit of Immunology, Rheumatology, Allergy and Rare Diseases (UnIRAR), IRCCS-San Raffaele Scientific Institute, Milan, Italy
39Vita-Salute San Raffaele University, Milan, Italy
Adriana Cariddi
7Unit of Immunology, Rheumatology, Allergy and Rare Diseases (UnIRAR), IRCCS-San Raffaele Scientific Institute, Milan, Italy
Paola Toniati
8Unit of Rheumatology and Clinical Immunology, University and ASST Spedali Civili, Brescia, Italy
Silvia Tamanini
8Unit of Rheumatology and Clinical Immunology, University and ASST Spedali Civili, Brescia, Italy
Federica Furini
9Dept of Medical Sciences, University of Ferrara, Ferrara, Italy
10Rheumatology Unit, Azienda Ospedaliero-Universitaria S. Anna, Ferrara, Italy
Alessandra Bortoluzzi
9Dept of Medical Sciences, University of Ferrara, Ferrara, Italy
10Rheumatology Unit, Azienda Ospedaliero-Universitaria S. Anna, Ferrara, Italy
Elisa Tinazzi
11Dept of Medicine, University of Verona, Verona, Italy
Lorenzo Delfino
11Dept of Medicine, University of Verona, Verona, Italy
Iuliana Badiu
12Allergy and Pneumology Unit, A.O.S. Croce e Carle, Cuneo, Italy
Giovanni Rolla
40Dept of Medical Science, Allergy and Clinical Immunology, University of Torino and AO Ordine Mauriziano Umberto I, Turin, Italy
Vincenzo Venerito
13Rheumatology Unit, Dept of Emergency and Organ Transplantation (DETO), Polyclinic Hospital, University of Bari, Bari, Italy
Florenzo Iannone
13Rheumatology Unit, Dept of Emergency and Organ Transplantation (DETO), Polyclinic Hospital, University of Bari, Bari, Italy
Alvise Berti
14Dept of Rheumatology, Santa Chiara Hospital, Trento, Italy
Roberto Bortolotti
14Dept of Rheumatology, Santa Chiara Hospital, Trento, Italy
Vito Racanelli
15Dept of Biomedical Sciences and Human Oncology, Unit of Internal Medicine “Guido Baccelli”, University of Bari “Aldo Moro” Medical School, Bari, Italy
Guido Jeannin
16Nephrology Unit, ASST Spedali Civili, Brescia, Italy
Angela Padula
17Rheumatology Dept of Lucania, San Carlo Hospital, Potenza, Italy
Alberto Cauli
18Rheumatology, Dept of Medical Sciences and Public Health, University Clinic, Cagliari, Italy
Roberta Priori
19Rheumatology Unit, Dept of Clinical Internal, Anesthesiological and Cardiovascular Sciences, Sapienza University of Rome, Rome, Italy
Armando Gabrielli
41Dept of Internal Medicine, Università Politecnica delle Marche, Ancona, Italy
Milena Bond
14Dept of Rheumatology, Santa Chiara Hospital, Trento, Italy
21Rheumatology Clinic, Dept of Medicine (DAME), University of Udine, Udine, Italy
Martina Tedesco
16Nephrology Unit, ASST Spedali Civili, Brescia, Italy
42Dept of Biomedical and Clinical Sciences “L. Sacco”, University of Milan, Milan, Italy
Giulia Pazzola
24Azienda USL-IRCCS di Reggio Emilia and University of Modena and Reggio Emilia, Reggio Emilia, Italy
Paola Tomietto
25Rheumatology Unit, Internal Medicine Dept, Cattinara Teaching Hospital (ASUITS), Trieste, Italy
Marco Pellecchio
43Struttura Complessa Medicina Interna 1 P.O. Levante, ASL 2 Savona, Savona, Italy
Chiara Marvisi
24Azienda USL-IRCCS di Reggio Emilia and University of Modena and Reggio Emilia, Reggio Emilia, Italy
44Nephrology Unit, University Hospital, Parma, Italy
Federica Maritati
45Dept of Experimental Diagnostic and Specialty Medicine (DIMES), Nephrology, Dialysis and Renal Transplant Unit, St. Orsola Hospital, University of Bologna, Bologna, Italy
Alessandra Palmisano
44Nephrology Unit, University Hospital, Parma, Italy
Christian Dejaco
46Hospital of Brunico (SABES-ASDAA), Dept of Rheumatology, Brunico, Italy
47Dept of Rheumatology and Immunology, Medical University Graz, Graz, Austria
Johann Willeit
48Dept of Neurology, Medical University of Innsbruck, Innsbruck, Austria
Stefan Kiechl
48Dept of Neurology, Medical University of Innsbruck, Innsbruck, Austria
Iacopo Olivotto
1Dept of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy
49Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy
Peter Willeit
48Dept of Neurology, Medical University of Innsbruck, Innsbruck, Austria
50Dept of Public Health and Primary Care, University of Cambridge, Cambridge, UK
53These authors contributed equally to this manuscript
Domenico Prisco
1Dept of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy
53These authors contributed equally to this manuscript
Augusto Vaglio
51Nephrology and Dialysis Unit, Meyer Children's Hospital, Florence, Italy
52Dept of Experimental, Clinical and Biomedical Sciences “Mario Serio”, University of Firenze, Florence, Italy
53These authors contributed equally to this manuscript
Giacomo Emmi
1Dept of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy
53These authors contributed equally to this manuscript
Figures
Supplementary Materials
Vol 57 Issue 5
Table of Contents
Risk of acute arterial and venous thromboembolic events in eosinophilic granulomatosis with polyangiitis (Churg–Strauss syndrome)
Alessandra Bettiol, Renato Alberto Sinico, Franco Schiavon, Sara Monti, Enrica Paola Bozzolo, Franco Franceschini, Marcello Govoni, Claudio Lunardi, Giuseppe Guida, Giuseppe Lopalco, Giuseppe Paolazzi, Angelo Vacca, Gina Gregorini, Pietro Leccese, Matteo Piga, Fabrizio Conti, Paolo Fraticelli, Luca Quartuccio, Federico Alberici, Carlo Salvarani, Silvano Bettio, Simone Negrini, Carlo Selmi, Savino Sciascia, Gabriella Moroni, Loredana Colla, Carlo Manno, Maria Letizia Urban, Alfredo Vannacci, Maria Rosa Pozzi, Paolo Fabbrini, Stefano Polti, Mara Felicetti, Maria Rita Marchi, Roberto Padoan, Paolo Delvino, Roberto Caporali, Carlomaurizio Montecucco, Lorenzo Dagna, Adriana Cariddi, Paola Toniati, Silvia Tamanini, Federica Furini, Alessandra Bortoluzzi, Elisa Tinazzi, Lorenzo Delfino, Iuliana Badiu, Giovanni Rolla, Vincenzo Venerito, Florenzo Iannone, Alvise Berti, Roberto Bortolotti, Vito Racanelli, Guido Jeannin, Angela Padula, Alberto Cauli, Roberta Priori, Armando Gabrielli, Milena Bond, Martina Tedesco, Giulia Pazzola, Paola Tomietto, Marco Pellecchio, Chiara Marvisi, Federica Maritati, Alessandra Palmisano, Christian Dejaco, Johann Willeit, Stefan Kiechl, Iacopo Olivotto, Peter Willeit, Domenico Prisco, Augusto Vaglio, Giacomo Emmi
European Respiratory Journal May 2021, 57 (5) 2004158; DOI: 10.1183/13993003.04158-2020
Risk of acute arterial and venous thromboembolic events in eosinophilic granulomatosis with polyangiitis (Churg–Strauss syndrome)
Alessandra Bettiol, Renato Alberto Sinico, Franco Schiavon, Sara Monti, Enrica Paola Bozzolo, Franco Franceschini, Marcello Govoni, Claudio Lunardi, Giuseppe Guida, Giuseppe Lopalco, Giuseppe Paolazzi, Angelo Vacca, Gina Gregorini, Pietro Leccese, Matteo Piga, Fabrizio Conti, Paolo Fraticelli, Luca Quartuccio, Federico Alberici, Carlo Salvarani, Silvano Bettio, Simone Negrini, Carlo Selmi, Savino Sciascia, Gabriella Moroni, Loredana Colla, Carlo Manno, Maria Letizia Urban, Alfredo Vannacci, Maria Rosa Pozzi, Paolo Fabbrini, Stefano Polti, Mara Felicetti, Maria Rita Marchi, Roberto Padoan, Paolo Delvino, Roberto Caporali, Carlomaurizio Montecucco, Lorenzo Dagna, Adriana Cariddi, Paola Toniati, Silvia Tamanini, Federica Furini, Alessandra Bortoluzzi, Elisa Tinazzi, Lorenzo Delfino, Iuliana Badiu, Giovanni Rolla, Vincenzo Venerito, Florenzo Iannone, Alvise Berti, Roberto Bortolotti, Vito Racanelli, Guido Jeannin, Angela Padula, Alberto Cauli, Roberta Priori, Armando Gabrielli, Milena Bond, Martina Tedesco, Giulia Pazzola, Paola Tomietto, Marco Pellecchio, Chiara Marvisi, Federica Maritati, Alessandra Palmisano, Christian Dejaco, Johann Willeit, Stefan Kiechl, Iacopo Olivotto, Peter Willeit, Domenico Prisco, Augusto Vaglio, Giacomo Emmi
European Respiratory Journal May 2021, 57 (5) 2004158; DOI: 10.1183/13993003.04158-2020