Ambrisentan | Endothelin receptor antagonist | Negative | NCT00768300 | Not published | December 2008–February 2011 |
BIBF 1120 | Inhibitor of VEGF, PDGF, FGF receptor kinases | Positive | NCT00514683 | Preventative and therapeutic | August 2007–June 2010 |
Bosentan | Endothelin receptor antagonist | Negative Negative | NCT00071461 NCT00391443 | Preventative and therapeutic | August 2003–May 2010 February 2007–July 2010 |
CNTO-888 | Anti-CCL2 antibody | Negative | NCT00786201 | Not published | December 2008–January 2012 |
Etanercept | TNF-α receptor antagonist | Negative | NCT00063869 | Not published | July 2003–March 2005 |
FG-3019 | Antibody against CTGF | Results awaited Positive (Phase I) Results awaited | NCT00074698 NCT01262001 NCT01890265 | Preventative | December 2003–May 2004 March 2011–June 2017 June 2013–November 2017 |
GC1008 | TGF-β neutralising antibody | Results awaited | NCT00125385 | Not published | July 2005–September 2008 |
GS6624 | Antibody against LOXL2 | Results awaited | NCT01362231 | Not published | December 2010–December 2012 |
Imatinib | Tyrosine kinase inhibitor | Negative | NCT00131274 | Preventative and therapeutic | April 2003–August 2007 |
Interferon-γ | Anti-inflammatory | Negative Negative | NCT00047645 NCT00075998 | Not published | April 2000–December 2002 December 2003–May 2007 |
Macitentan | Endothelin receptor antagonist | Negative | NCT00903331 | Not published | May 2009–August 2011 |
NAC | Antioxidant | Negative | NCT00650091 | Preventative | October 2009–January 2014 |
NAC, azathioprine, prednisone | Antioxidant | Positive Negative | NCT00639496 NCT00650091 | Not published | March 2000–July 2003 October 2009–January 2014 |
Pirfenidone | Antifibrotic | Positive/Negative Positive Positive | NCT00287716 JAPICCTCI-050121 NCT01366209 | Preventative and therapeutic | July 2006–November 2008 Not stated June 2011–February 2014 |
QAX576 | Anti-IL-13 antibody | Negative | NCT01266135 | Not published | December 2010–April 2013 |
Warfarin | Anticoagulants | Negative | NCT00957242 | Not published | October 2009–July 2011 |