Predictor | Overall cohort HR (95% CI; p-value) | PAH-SSc HR (95% CI; p-value) | IPAH HR (95% CI; p-value) |
Age | 1.00 (0.97–1.03; 0.90) | 1.01 (0.97–1.04; 0.78) | 0.97 (0.91–1.03; 0.28) |
Race | 1.31 (0.60–2.86; 0.49) | 2.92 (1.14–7.45; 0.03) | 0.48 (0.09–2.49; 0.38) |
Sex | 0.79 (0.27–2.31; 0.67) | 1.02 (0.24–4.42; 0.98) | 0.45 (0.08–2.45; 0.36) |
BMI | 0.93 (0.86–0.99; 0.04) | 0.92 (0.84–1.00; 0.08) | 0.98 (0.86–1.11; 0.71) |
NYHA | 2.58 (1.47–4.49; <0.01) | 2.76 (1.37–5.52; <0.01) | 1.95 (0.73–5.17; 0.18) |
6MWD | 0.99 (0.99–1.00; 0.01) | 0.99 (0.99–1.00; 0.17) | 0.99 (0.99–1.00; 0.05) |
eGFR | 1.00 (0.98–1.01; 0.60) | 0.99 (0.98–1.01; 0.69) | 0.99 (0.96–1.03; 0.78) |
Treatment status | 0.97 (0.36–2.07; 0.95) | 1.52 (0.62–3.66; 0.35) | 0.48 (0.10–2.17; 0.34) |
Disease duration | 0.99 (0.99–0.99; <0.01) | 0.99 (0.99–0.99;<0.01) | 0.99 (0.99–0.99; 0.03) |
Duration prior to proBNP | 0.99 (0.99–1.00; 0.38) | 1.00 (0.99–1.00; 0.56) | 0.99 (0.99–1.00; 0.31) |
Pra | 1.07 (1.00–1.15; 0.04) | 1.05 (0.98–1.14; 0.15) | 1.12 (0.99–1.28; 0.08) |
P̄pa | 1.02 (0.99–1.05; 0.11) | 1.03 (0.99–1.07; 0.07) | 1.03 (0.98–1.09; 0.21) |
Cardiac index | 0.32 (0.17–0.63;<0.01) | 0.32 (0.15–0.67; <0.01) | 0.42 (0.11–0.57; 0.01) |
PCWP | 0.94 (0.85–1.06; 0.36) | 0.96 (0.86–1.07; 0.41) | 0.95 (0.75–1.20; 0.67) |
PVR | 1.16 (1.09–1.24;<0.01) | 1.17 (1.09–1.27;<0.01) | 1.18 (1.06–1.33;<0.01) |
PA sat | 0.93 (0.89–0.97; <0.01) | 0.92 (0.88–0.96; <0.01) | 0.96 (0.87–1.04; 0.30) |
NT-proBNP log10 | 3.18 (1.60–6.33;<0.01) | 3.07 (1.35–7.00; <0.01) | 2.02 (0.55–7.52; 0.29) |