| Total | dcSSc | lcSSc |
Subjects n | 105 | 45 | 60 |
Final PFT results | | | |
FVC <80% pred | 34 (32.4) | 23 (50.0) | 10 (16.9) |
FVC ≤50% pred | 9 (8.5) | 9 (19.6) | 0 (0.0) |
DL,CO <80% pred¶ | 81 (82.7) | 33 (71.7) | 48 (31.4) |
PFT outcome | | | |
FVC decline ≥10% pred | 29 (27.6) | 21 (45.7) | 8 (13.6) |
FVC decline ≥20% pred | 19 (18.1) | 13 (28.3) | 6 (10.2) |
DL,CO decline ≥15% pred | 39 (39.8) | 14 (30.4) | 25 (42.4) |
FVC decline ≥10% pred or DL,CO decline ≥15% pred | 55 (52.4) | 26 (56.5) | 29 (49.2) |
Overall severity at end of follow-up+ | | | |
Final Medsger stage ≥3 | 39 (37.5) | 25 (54.3) | 14 (23.7) |
Overall aggravation of SSc | 36 (34.6) | 22 (27.8) | 14 (23.7) |