Type | Characteristic components of lesion | Proportional incidence % | Appearances | Other features |
0 | Tracheobronchial | 1–3 | Solid | Neonates, poor prognosis |
1 | Bronchial/bronchiolar | 60–70 | Large cysts (≤10 cm) | Delayed presentation |
2 | Bronchiolar | 10–15 | Multiple small cysts (≤2 cm) | Neonates, poor prognosis |
3 | Bronchiolar/alveolar | 5 | Solid | Neonates, poor prognosis |
4 | Distal acinar | 15 | Large cysts (≤10 cm) | Neonates and infants, good prognosis |