Interstitial and orphan lung disease

Long-term outcomes of adult pulmonary Langerhans cell histiocytosis: a prospective cohort
Amira Benattia, Emmanuelle Bugnet, Anouk Walter-Petrich, Constance de Margerie-Mellon, Véronique Meignin, Agathe Seguin-Givelet, Gwenaël Lorillon, Sylvie Chevret, Abdellatif Tazi

European Respiratory Journal May 2022, 59 (5) 2101017; DOI: 10.1183/13993003.01017-2021
Computed tomography-based radiomics decodes prognostic and molecular differences in interstitial lung disease related to systemic sclerosis
Janine Schniering, Malgorzata Maciukiewicz, Hubert S. Gabrys, Matthias Brunner, Christian Blüthgen, Chantal Meier, Sophie Braga-Lagache, Anne-Christine Uldry, Manfred Heller, Matthias Guckenberger, Håvard Fretheim, Christos T. Nakas, Anna-Maria Hoffmann-Vold, Oliver Distler, Thomas Frauenfelder, Stephanie Tanadini-Lang, Britta Maurer

European Respiratory Journal May 2022, 59 (5) 2004503; DOI: 10.1183/13993003.04503-2020
Nestin promotes pulmonary fibrosis via facilitating recycling of TGF-β receptor I
Jiancheng Wang, Xiaofan Lai, Senyu Yao, Hainan Chen, Jianye Cai, Yulong Luo, Yi Wang, Yuan Qiu, Yinong Huang, Xiaoyue Wei, Boyan Wang, Qiying Lu, Yuanjun Guan, Tao Wang, Shiyue Li, Andy Peng Xiang

European Respiratory Journal May 2022, 59 (5) 2003721; DOI: 10.1183/13993003.03721-2020
Intracellular hydroxyproline imprinting following resolution of bleomycin-induced pulmonary fibrosis
Shengren Song, Zhenli Fu, Ruijuan Guan, Jie Zhao, Penghui Yang, Yang Li, Hang Yin, Yunxin Lai, Gencheng Gong, Simin Zhao, Jiangtian Yu, Xiaomin Peng, Ying He, Yumei Luo, Nanshan Zhong, Jin Su

European Respiratory Journal May 2022, 59 (5) 2100864; DOI: 10.1183/13993003.00864-2021
Methionine supplementation for multi-organ dysfunction in MetRS-related pulmonary alveolar proteinosis
Alice Hadchouel, David Drummond, Clément Pontoizeau, Laura Aoust, Maria-Margarita Hurtado Nedelec, Jamel El Benna, Elsa Gachelin, Caroline Perisson, Clémentine Vigier, Manuel Schiff, Florence Lacaille, Thierry Jo Molina, Laureline Berteloot, Sylvain Renolleau, Chris Ottolenghi, Jean-Marc Tréluyer, Jacques de Blic, Christophe Delacourt

European Respiratory Journal Apr 2022, 59 (4) 2101554; DOI: 10.1183/13993003.01554-2021
Protease activity sensors enable real-time treatment response monitoring in lymphangioleiomyomatosis
Jesse D. Kirkpatrick, Ava P. Soleimany, Jaideep S. Dudani, Heng-Jia Liu, Hilaire C. Lam, Carmen Priolo, Elizabeth P. Henske, Sangeeta N. Bhatia

European Respiratory Journal Apr 2022, 59 (4) 2100664; DOI: 10.1183/13993003.00664-2021
Ex vivo delivery of regulatory T-cells for control of alloimmune priming in the donor lung
Ei Miyamoto, Akihiro Takahagi, Akihiro Ohsumi, Tereza Martinu, David Hwang, Kristen M. Boonstra, Betty Joe, Juan Mauricio Umana, Ke F. Bei, Daniel Vosoughi, Mingyao Liu, Marcelo Cypel, Shaf Keshavjee, Stephen C. Juvet

European Respiratory Journal Apr 2022, 59 (4) 2100798; DOI: 10.1183/13993003.00798-2021
Biomarker signatures for progressive idiopathic pulmonary fibrosis
Britt Clynick, Tamera J. Corte, Helen E. Jo, Iain Stewart, Ian N. Glaspole, Christopher Grainge, Toby M. Maher, Vidya Navaratnam, Richard Hubbard, Peter M.A. Hopkins, Paul N. Reynolds, Sally Chapman, Christopher Zappala, Gregory J. Keir, Wendy A. Cooper, Annabelle M. Mahar, Samantha Ellis, Nicole S. Goh, Emma De Jong, Lilian Cha, Dino B.A. Tan, Lucy Leigh, Christopher Oldmeadow, E. Haydn Walters, R. Gisli Jenkins, Yuben Moodley

European Respiratory Journal Mar 2022, 59 (3) 2101181; DOI: 10.1183/13993003.01181-2021
Nintedanib in progressive interstitial lung diseases: data from the whole INBUILD trial
Kevin R. Flaherty, Athol U. Wells, Vincent Cottin, Anand Devaraj, Yoshikazu Inoue, Luca Richeldi, Simon L.F. Walsh, Martin Kolb, Dirk Koschel, Teng Moua, Susanne Stowasser, Rainer-Georg Goeldner, Rozsa Schlenker-Herceg, Kevin K. Brown

European Respiratory Journal Mar 2022, 59 (3) 2004538; DOI: 10.1183/13993003.04538-2020
Genetically increased circulating FUT3 level leads to reduced risk of idiopathic pulmonary fibrosis: a Mendelian randomisation study
Tomoko Nakanishi, Agustin Cerani, Vincenzo Forgetta, Sirui Zhou, Richard J. Allen, Olivia C. Leavy, Masaru Koido, Deborah Assayag, R. Gisli Jenkins, Louise V. Wain, Ivana V. Yang, G. Mark Lathrop, Paul J. Wolters, David A. Schwartz, J. Brent Richards

European Respiratory Journal Feb 2022, 59 (2) 2003979; DOI: 10.1183/13993003.03979-2020

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