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CF and non-CF bronchiectasis

  • Impact of a high emergency lung transplantation programme for cystic fibrosis in France: insight from a comparison with Canada
    Adèle Coriati, Jenna Sykes, Lydie Lemonnier, Xiayi Ma, Sanja Stanojevic, Clémence Dehillotte, Nicolas Carlier, Anne L. Stephenson, Pierre-Régis Burgel
    European Respiratory Journal Jan 2022, 59 (1) 2100014; DOI: 10.1183/13993003.00014-2021
  • Theratyping cystic fibrosis in vitro in ALI culture and organoid models generated from patient-derived nasal epithelial conditionally reprogrammed stem cells
    Giovanni Sette, Stefania Lo Cicero, Giovanna Blaconà, Silvia Pierandrei, Sabina Maria Bruno, Valentina Salvati, Germana Castelli, Mario Falchi, Benedetta Fabrizzi, Giuseppe Cimino, Ruggero De Maria, Mauro Biffoni, Adriana Eramo, Marco Lucarelli
    European Respiratory Journal Dec 2021, 58 (6) 2100908; DOI: 10.1183/13993003.00908-2021
  • SPLUNC1: a novel marker of cystic fibrosis exacerbations
    Sara Khanal, Megan Webster, Naiqian Niu, Jana Zielonka, Myra Nunez, Geoffrey Chupp, Martin D. Slade, Lauren Cohn, Maor Sauler, Jose L. Gomez, Robert Tarran, Lokesh Sharma, Charles S. Dela Cruz, Marie Egan, Theresa Laguna, Clemente J. Britto
    European Respiratory Journal Nov 2021, 58 (5) 2000507; DOI: 10.1183/13993003.00507-2020
  • Psychometrics of health-related quality of life questionnaires in bronchiectasis: a systematic review and meta-analysis
    Rebecca H. McLeese, Arietta Spinou, Zina Alfahl, Michail Tsagris, J. Stuart Elborn, James D. Chalmers, Anthony De Soyza, Michael R. Loebinger, Surinder S. Birring, Konstantinos C. Fragkos, Robert Wilson, Katherine O'Neill, Judy M. Bradley
    European Respiratory Journal Nov 2021, 58 (5) 2100025; DOI: 10.1183/13993003.00025-2021
  • The risk of community-acquired pneumonia in children using gastric acid suppressants
    Linda J.T.M. van der Sande, Quirijn Jöbsis, Michiel A.G.E. Bannier, Ewoudt M.W. van de Garde, Jan J.M. Coremans, Frank de Vries, Edward Dompeling, Johanna H.M. Driessen
    European Respiratory Journal Oct 2021, 58 (4) 2003229; DOI: 10.1183/13993003.03229-2020
  • Survival estimates in European cystic fibrosis patients and the impact of socioeconomic factors: a retrospective registry cohort study
    Edward F. McKone, Cono Ariti, Abaigeal Jackson, Anna Zolin, Siobhán B. Carr, Annalisa Orenti, Jacqui G. van Rens, Lydie Lemonnier, Milan Macek, Ruth H. Keogh, Lutz Naehrlich
    European Respiratory Journal Sep 2021, 58 (3) 2002288; DOI: 10.1183/13993003.02288-2020
  • Unsupervised phenotypic clustering for determining clinical status in children with cystic fibrosis
    Nicole Filipow, Gwyneth Davies, Eleanor Main, Neil J. Sebire, Colin Wallis, Felix Ratjen, Sanja Stanojevic
    European Respiratory Journal Aug 2021, 58 (2) 2002881; DOI: 10.1183/13993003.02881-2020
  • Determinants of lung disease progression measured by lung clearance index in children with cystic fibrosis
    Sanja Stanojevic, Stephanie D. Davis, Lucy Perrem, Michelle Shaw, George Retsch-Bogart, Miriam Davis, Renee Jensen, Charles C. Clem, Sarah M. Isaac, Julia Guido, Sylvia Jara, Lisa France, Nancy McDonald, Melinda Solomon, Neil Sweezey, Hartmut Grasemann, Valerie Waters, D.B. Sanders, Felix A. Ratjen
    European Respiratory Journal Jul 2021, 58 (1) 2003380; DOI: 10.1183/13993003.03380-2020
  • TLR2-mediated innate immune priming boosts lung anti-viral immunity
    Jason Girkin, Su-Ling Loo, Camille Esneau, Steven Maltby, Francesca Mercuri, Brendon Chua, Andrew T. Reid, Punnam Chander Veerati, Chris L. Grainge, Peter A.B. Wark, Darryl Knight, David Jackson, Christophe Demaison, Nathan W. Bartlett
    European Respiratory Journal Jul 2021, 58 (1) 2001584; DOI: 10.1183/13993003.01584-2020
  • IL-17A from innate and adaptive lymphocytes contributes to inflammation and damage in cystic fibrosis lung disease
    Matthias Hagner, Melanie Albrecht, Matteo Guerra, Peter Braubach, Olga Halle, Zhe Zhou-Suckow, Simone Butz, Danny Jonigk, Gesine Hansen, Carsten Schultz, Anna-Maria Dittrich, Marcus A. Mall
    European Respiratory Journal Jun 2021, 57 (6) 1900716; DOI: 10.1183/13993003.00716-2019

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