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CF and non-CF bronchiectasis

  • Prevalence, risk factors and outcomes of cardiac disease in cystic fibrosis: a multinational retrospective cohort study
    Freddy Frost, Dilip Nazareth, Laurent Fauchier, Dennis Wat, James Shelley, Philip Austin, Martin J. Walshaw, Gregory Y.H. Lip
    European Respiratory Journal Oct 2023, 62 (4) 2300174; DOI: 10.1183/13993003.00174-2023
  • Theratyping cystic fibrosis patients to guide elexacaftor/tezacaftor/ivacaftor out-of-label prescription
    Elise Dreano, Pierre Régis Burgel, Aurelie Hatton, Naim Bouazza, Benoit Chevalier, Julie Macey, Sylvie Leroy, Isabelle Durieu, Laurence Weiss, Dominique Grenet, Nathalie Stremler, Camille Ohlmann, Philippe Reix, Michele Porzio, Pauline Roux Claude, Natacha Rémus, Benoit Douvry, Sylvie Montcouquiol, Laure Cosson, Julie Mankikian, Jeanne Languepin, Veronique Houdouin, Laurence Le Clainche, Anne Guillaumot, Delphine Pouradier, Adrien Tissot, Pascaline Priou, Laurent Mély, Frederique Chedevergne, Muriel Lebourgeois, Jean Lebihan, Clémence Martin, Flora Zavala, Jennifer Da Silva, Lydie Lemonnier, Mairead Kelly-Aubert, Anita Golec, Pierre Foucaud, Christophe Marguet, Aleksander Edelman, Alexandre Hinzpeter, Paola de Carli, Emmanuelle Girodon, Isabelle Sermet-Gaudelus, Iwona Pranke
    European Respiratory Journal Oct 2023, 62 (4) 2300110; DOI: 10.1183/13993003.00110-2023
  • Charting the path to expanded access for CFTR modulator drugs: the nose knows
    Christine Bear, Felix Ratjen
    European Respiratory Journal Oct 2023, 62 (4) 2301387; DOI: 10.1183/13993003.01387-2023
  • Real-world effectiveness of airway clearance techniques in children with cystic fibrosis
    Nicole Filipow, Sanja Stanojevic, Emma Raywood, Harriet Shannon, Gizem Tanriver, Kunal Kapoor, Helen Douglas, Gwyneth Davies, Rachel O'Connor, Nicky Murray, Eleanor Main
    European Respiratory Journal Sep 2023, 62 (3) 2300522; DOI: 10.1183/13993003.00522-2023
  • Longitudinal effects of elexacaftor/tezacaftor/ivacaftor on sputum viscoelastic properties, airway infection and inflammation in patients with cystic fibrosis
    Laura Schaupp, Annalisa Addante, Mirjam Völler, Kerstin Fentker, Aditi Kuppe, Markus Bardua, Julia Duerr, Linus Piehler, Jobst Röhmel, Stephanie Thee, Marieluise Kirchner, Matthias Ziehm, Daniel Lauster, Rainer Haag, Michael Gradzielski, Mirjam Stahl, Philipp Mertins, Sébastien Boutin, Simon Y. Graeber, Marcus A. Mall
    European Respiratory Journal Aug 2023, 62 (2) 2202153; DOI: 10.1183/13993003.02153-2022
  • European Respiratory Society statement on airway clearance techniques in adults with bronchiectasis
    Beatriz Herrero-Cortina, Annemarie L. Lee, Ana Oliveira, Brenda O'Neill, Cristina Jácome, Simone Dal Corso, William Poncin, Gerard Muñoz, Deniz Inal-Ince, Victoria Alcaraz-Serrano, Gregory Reychler, Angela Bellofiore, Annette Posthumus, Patient representative, Thomy Tonia, James D. Chalmers, Arietta Spinou
    European Respiratory Journal Jul 2023, 62 (1) 2202053; DOI: 10.1183/13993003.02053-2022
  • Saline at lower tonicity in cystic fibrosis (SALTI-CF) trial comparing 0.9% versus 3% versus 6% nebulised saline
    Tiffany J. Dwyer, Mark R. Elkins, Ruth Dentice, Samantha Forbes, Peter Cooper, Adam Jaffe, Jennifer Bishop, Peter G. Middleton, Peter Wark, Peter T.P. Bye
    European Respiratory Journal Jul 2023, 62 (1) 2100960; DOI: 10.1183/13993003.00960-2021
  • Implementation and evaluation of ultra-low dose CT in early cystic fibrosis lung disease
    Katie J. Bayfield, Oliver Weinheimer, Christie Boyton, Rachel Fitzpatrick, Anna Middleton, Brendan Kennedy, Anneliese Blaxland, Geshani Jayasuriya, Neil Caplain, Hana Issa, Robert Goetti, Mark O. Wielpütz, Lifeng Yu, Craig J. Galban, Terry E. Robinson, Brian Bartholmai, Dominic Fitzgerald, Hiran Selvadurai, Paul D. Robinson
    European Respiratory Journal Jul 2023, 62 (1) 2300286; DOI: 10.1183/13993003.00286-2023
  • A novel thiol-saccharide mucolytic for the treatment of muco-obstructive lung diseases
    Annalisa Addante, Wilfred Raymond, Irina Gitlin, Annabelle Charbit, Xavier Orain, Aaron Wolfe Scheffler, Aditi Kuppe, Julia Duerr, Maria Daniltchenko, Marika Drescher, Simon Y. Graeber, Anne-Marie Healy, Stefan Oscarson, John V. Fahy, Marcus A. Mall
    European Respiratory Journal May 2023, 61 (5) 2202022; DOI: 10.1183/13993003.02022-2022
  • The French compassionate programme of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis with advanced lung disease and no F508del CFTR variant
    Pierre-Régis Burgel, Isabelle Sermet-Gaudelus, Isabelle Durieu, Reem Kanaan, Julie Macey, Dominique Grenet, Michele Porzio, Nathalie Coolen-Allou, Raphael Chiron, Christophe Marguet, Benoit Douvry, Nadine Dufeu, Isabelle Danner-Boucher, Pierre Foucaud, Lydie Lemonnier, Emmanuelle Girodon, Jennifer Da Silva, Clémence Martin, on behalf of the French CF Reference Network study group, , Claire Andrejak, Pascaline Priou, Bénédicte Richaud-Thiriez, Julie Macey, Sylvie Montcouquiol, Benoit Douvry, Natacha Remus, Annlyse Fanton, Nathalie Coolen-Allou, Elsa Gachelin, Constance Vuillard, Camille Audousset, Louise Duthoit, Elisabeth Bellet-Fraysse, Jeanne Languepin, Isabelle Durieu, Raphaele Nove-Josserand, Camille Ohlmann, Quitterie Raynaud, Nadine Dufeu, Raphael Chiron, Yves Billon, Isabelle Danner-Boucher, Adrien Tissot, Sylvie Leroy, Frédérique Aubourg, Espérie Burnet, Pierre-Régis Burgel, Nicolas Carlier, Jennifer Da Silva, Isabelle Fajac, Emmanuelle Girodon, Reem Kanaan, Isabelle Honoré, Clémence Martin, Muriel Le Bourgeois, Isabelle Sermet-Gaudelus, Laurence Le Clainche-Viala, Harriet Corvol, Clémence Dehillotte, Pierre Foucaud, Lydie Lemonnier, Graziella Brinchault, Bruno Ravoninjatovo, Jean Le Bihan, Sophie Ramel, Christophe Marguet, Michele Porzio, Laurence Weiss, Dominique Grenet, Sandra de Miranda, Laure Cosson, Julie Mankikian, Delphine Pouradier
    European Respiratory Journal May 2023, 61 (5) 2202437; DOI: 10.1183/13993003.02437-2022

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  • Acute lung injury and critical care (83)
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