Asthma guidelines from the Global Initiative for Asthma (GINA) and from the National Heart,
Lung, and Blood Institute provide conflicting definitions of airflow obstruction, suggesting a …

AIM: Pulmonary involvement is not generally considered a main feature of Marfan syndrome,
an autosomal connective tissue disorder caused by mutations in fibrillin 1. Thanks to the …

The notion that the earliest manifestation of COPD is an increase in gas trapping, with a
decreasing VC that forces the FEV1 to decline with it, has been recently re-evaluated [1]. To …

… ) underwent lung function testing, CT densitometry and exhaled breath analysis by electronic
nose. Raw data from electronic nose were reduced to 8 principal components (PC). 32 vari…

… (D, E) Conventional radiography studies in patients D and E illustrate the respective
presence of a hiatal and diaphragmatic hernia. Color images are available online. …

… /FVC, forced expiratory flow between 25 and 75% of FVC (FEF25–75), total lung capacity
(TLC), residual volume (RV) and functional residual capacity (FRC) by means of electronic …

To assess the contribution of individual TGF-β isoforms to aortopathy in Marfan syndrome (MFS),
we quantified the survival and phenotypes of mice with a combined fibrillin1 (the gene …

Figure 2. High-resolution computed tomography of the chest with intravenous contrast
demonstrates extensive bilateral giant bullae, which are most pronounced in the bilateral upper …

Background: Marfan Syndrome (MFS) is an inherited connective tissue disorder caused by
mutations in the FBN1 (fibrillin-1) gene. Lung abnormalities are common in MFS, but their …

… I have obtained needed written permission statement(s) from the owner(s) of each third-party
copyrighted matter to be included in my work, allowing electronic distribution (if such use is …