Liver involvement in hereditary hemorrhagic telangiectasia: CT and clinical findings do not correlate in symptomatic patients

AJR Am J Roentgenol. 2006 Oct;187(4):W399-405. doi: 10.2214/AJR.05.1068.

Abstract

Objective: The purpose of our study was to report the multiphasic CT findings in patients with symptomatic liver involvement by hereditary hemorrhagic telangiectasia (HHT) and to correlate the CT findings with the type of clinical presentation.

Conclusion: Patients with symptomatic HHT liver disease have diffuse hepatic telangiectases, a dilated common hepatic artery, and a high incidence of biliary abnormalities. Multiphasic CT is useful in diagnosing liver involvement due to HHT; however, no strong correlation was seen between CT findings and the clinical subtype of HHT liver disease.

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Angiography
  • Female
  • Humans
  • Liver / blood supply
  • Liver Diseases / complications
  • Liver Diseases / diagnostic imaging*
  • Male
  • Middle Aged
  • Telangiectasia, Hereditary Hemorrhagic / complications*
  • Tomography, X-Ray Computed*