Table 1– Haemodynamic parameters at the time of diagnosis for children and adults with idiopathic or heitable pulmonary arterial hypertension
ParameterAdultsChildren
Subjects n6978
P̄pa mmHg56±1362±22
Mean SBP mmHg90±1375±12
Mean RAP mmHg10±75±3
Mean Sv,O2 %58±1064±9
Mean Sa,O2 %93±594±4
PVR index U·m225±1520±13
SVR index U·m239±1824±11
P̄pcw mmHg9±58±4
CI# L·min−1·m21.9±1.72.8±1.2

  • Data are presented as mean±sd unless otherwise stated. Paediatric and adult patients were consecutively enrolled in one centre between 1991 and 2005. P̄pa: mean pulmonary artery pressure; SBP: systemic blood pressure; RAP: right arterial pressure; Sv,O2: mixed venous oxygen saturation; Sa,O2: arterial oxygen saturation; PVR: pulmonary vascular resistance; SVR: systemic vascular resistance; P̄pcw: mean pulmonary capillary wedge pressure; CI: cardiac index. #: n = 129. Reproduced and modified from 80 with permission from the publisher.