Table 1—

Haemodynamic profiles in patients with hereditary haemorrhagic telangiectasia and pulmonary hypertension(PH)

ProfilepaCOPAOPTPGPVR
PH, high flow, LV failure↑↑High-normal or ↑NormalNormal
PAH↑↑Normal↑↑
  • pa: mean pulmonary arterial pressure; CO: cardiac output; PAOP: pulmonary artery occlusion pressure; TPG: transpulmonary gradient; PVR: pulmonary vascular resistance; LV: left ventricular; PAH: pulmonary arterial hypertension; ↑: increase; ↑↑: large increase; ↓: decrease.