Table 1—

New cases of neurofibromatosis with diffuse lung disease

Case No.	Clinical			Pulmonary function				HRCT
	Age yrs	Sex	Smoker	FVC	FEV₁	Ratio	D_L,CO
1	66	Male	Former	4.7 (98)	2.9 (78)	0.61	8.24 (24)	Upper lobe predominance of thin-walled cysts (fig. 1)
2	53	Male	Former	4.2 (95)	1.3 (41)	0.43	5.7 (15)	Bilateral asymmetric bullae (fig. 2)
3	70	Female	Never	N/A	N/A	N/A	N/A	Scattered upper lobe cysts (fig. 3)

Data are presented as n or n (%). HRCT: high-resolution computed tomography; FVC: forced vital capacity; FEV₁: forced expiratory volume in one second; D_L,CO: diffusing capacity of the lung for carbon monoxide; N/A: not applicable.