Table 1—

Numbers and probabilities (a priori probability) of final diagnoses in the group with suspected interstitial lung disease (ILD)

DiagnosisAll patientsSmokers
Sarcoidosis239 (33.7)19 (19.6)
UIP112 (15.8)16 (16.5)
EAA66 (9.3)4 (4.1)
NSIP46 (6.5)7 (7.2)
Tumour29 (4.1)11 (11.3)
Others25 (3.5)4 (4.1)
No fibrosis23 (3.2)2 (2.1)
Connective tissue disease18 (2.5)1 (1.0)
BOOP17 (2.4)
Histiocytosis X15 (2.1)9 (9.3)
Alveolar haemorrhage8 (1.1)1 (1.0)
Tuberculosis7 (1.0)1 (1.0)
Pneumoconiosis7 (1.0)2 (2.1)
Drug-induced alveolitis5 (0.7)
CEP4 (0.6)2 (2.1)
RBILD4 (0.6)1 (1.0)
Wegener's granulomatosis3 (0.4)
LIP3 (0.4)
Pneumocystis carinii1 (0.1)1 (1.0)
Alveolar proteinosis1 (0.1)
DIP1 (0.1)
Inflammatory disease76 (10.7)15 (16.4)
  • Data are presented as n (%). Only smokers with reliable information on current smoking at the time of diagnosis were analysed separately. UIP: usual interstitial pneumonia; EAA: extrinsic allergic alveolitis; NSIP: nonspecific interstitial pneumonia; others: e.g. obstructive sleep apnoea and cardiac failure; no fibrosis: neither ILD nor inflammatory disease nor tumour (e.g. persistent cough of unknown origin, suspected aspiration, reflux); BOOP: bronchiolitis obliterans organising pneumonia; CEP: chronic eosinophilic pneumonia; RBILD: respiratory bronchiolitis-associated interstitial lung disease; LIP: lymphocytic interstitial pneumonia; DIP: desquamative interstitial pneumonia