Category of congenital heart disease (CHD) in 40 adults and 66 children with pulmonary arterial hypertension, number of repaired CHD, and presence of bone morphogenetic protein receptor (BMPR)-2 mutations
| Adults | Children | |||||
| Total | Repaired | BMPR2 | Total | Repaired | BMPR2 | |
| Patent ductus arteriosus | 2 | 0 | 0 | 6 | 3 | 0 |
| ASD | 17 | 7 | 0 | 21 | 5 | 1# |
| ASD/PAPVR | 3 | 0 | 0 | 0 | 0 | 1# |
| Ventricular septal defect | 8 | 1 | 0 | 15 | 8 | 0 |
| PAPVR | 1 | 0 | 0 | 3 | 2 | 0 |
| Transposition of the great vessels | 3 | 3 | 0 | 7 | 3 | 0 |
| Atrial ventricular canal | 4 | 1 | 3 | 6 | 3 | 0 |
| Rare | 2 | 0 | 0 | 8 | 5 | 1 |
| Total | 40 | 12 | 3 | 66 | 29 | 3 |
Data are presented as n
ASD: atrial septal defect
PAPVR: partial anomalous pulmonary venous return
#: both CHDs had patent ductus arteriosus