Table 1—

Histological and clinical classification of idiopathic interstitial pneumonias#

HISTOLOGICAL PATTERNSClinical, Radiological, Pathological diagnoses
Usual interstitial pneumoniaIdiopathic pulmonary fibrosis/cryptogenic fibrosing alveolitis
Nonspecific interstitial pneumoniaNonspecific interstitial pneumonia (provisional)
Organizing pneumoniaCryptogenic organizing pneumonia+
Diffuse alveolar damageAcute interstitial pneumonia
Respiratory bronchiolitisRespiratory bronchiolitis interstitial lung disease
Desquamative interstitial pneumoniaDesquamative interstitial pneumonia
Lymphocytic interstitial pneumoniaLymphocytic interstitial pneumonia
  • #: Unclassifiable interstitial pneumonia: some cases are unclassifiable for a variety of reasons

  • : This group represents a heterogeneous group with poorly characterized clinical and radiological features that need further study

  • +: COP is the preferred term, but is synonymous with idiopathic bronchiolitis obliterans organizing pneumonia