Table 1

Treatment administered to 161 patients with usual interstitial pneumonia (UIP), nonspecific interstitial pneumonia (NSIP) and respiratory bronchiolitis interstitial lung disease/desquamative interstitial pneumonia (RBILD/DIP)

Treatment regimenUIPNSIPRBILD/DIP
n (%)n (%)n (%)
None7 (7)2 (6)2 (9)
Prednisone alone*35 (33)18 (55)10 (46)
Prednisone+azathioprine or cyclophosphamide31 (29)4 (12)6 (27)
Zileuton21 (20)4 (12)0 (0)
Azathioprine alone5 (4)4 (12)1 (4)
Miscellaneous7 (7)1 (3)3 (14)
  • *: 39 of the patients with UIP and NSIP received prednisone as part of a prospective study of high-dose steroids in idiopathic pulmonary fibrosis (see Therapy section for details)