Diagnosis | N (%) |
---|---|
Amyotrophic Lateral Sclerosis | 16 (59) |
Duchenne Muscular Dystrophy | 10 (37) |
Worster-Drought Syndrome | 1 (4) |
FVC | |
>500ml | 6 (22) |
<500ml | 4 (15) |
Unable to perform FVC | 17 (63) |
Pre-Operative Ventilatory Support | |
Nocturnal NIV | 13 (48) |
Diurnal NIV | 6 (22) |
24-hour NIV | 4 (15) |
Tracheostomy-ventilation (T-IPPV) | 4 (15) |