PT  - JOURNAL ARTICLE
AU  - Wiam Elkhattabi
AU  - Abdelaziz Aichane
AU  - Hasna Jabri
AU  - Regis Bopaka
AU  - Hicham Afif
AU  - Zoubida Bouayad
TI  - Thoracic determination of Behçet's disease
DP  - 2013 Sep 01
TA  - European Respiratory Journal
PG  - P1544
VI  - 42
IP  - Suppl 57
4099  - http://erj.ersjournals.com/content/42/Suppl_57/P1544.short
4100  - http://erj.ersjournals.com/content/42/Suppl_57/P1544.full
SO  - Eur Respir J2013 Sep 01; 42
AB  - Bechet's disease is a multisystemic vascularitis of unknown etiology. Thoracic lesions are dominated by venous and arterial diseases.We analyzed all cases of Behçet's disease with thoracic lesions identified between January 1997 and June 2012.The study included 21 patients. The average age was 34 years with a male predominance (86%). Six patients were followed for Behçet's disease previously.Hemoptysis and superior vena cava syndrome were the most common signs. Chest CT has confirmed thrombosis of the superior vena cava in 15 patients, and pulmonary artery aneurisms in 6 patients, three of them were complicated by thrombosis. Patients followed for thrombosis of the superior vena cava received anticoagulant therapy, corticosteroid and / or immunosuppressive therapy.The combination of corticosteroids, colchicine and / or immunosuppressive drugs were prescribed in patients with pulmonary aneurysms before surgical treatment. The main cause of death was massive hemoptysis, two patients has died immediately after diagnosis.Thoracic lesions of Behcet’s disease are not rare in Mediterranean countries, diagnosis is easy with CT, but there’s a lake in treatment. In these cases, prognosis is conditioned by thoracic lesions.