TY - JOUR T1 - Sinonasal mucoceles in cystic fibrosis JF - European Respiratory Journal JO - Eur Respir J VL - 42 IS - Suppl 57 SP - P1184 AU - Maurizio Di Cicco AU - Nicola Luca AU - Lorenzo Pignataro AU - Carla Colombo Y1 - 2013/09/01 UR - http://erj.ersjournals.com/content/42/Suppl_57/P1184.abstract N2 - IntroductionParanasal sinus mucoceles are a rare complication of rhinosinusitis in children. They consist in cystic formations with a wall of respiratory epithelium; their growth erode the bone walls with potential involvement of cranial structures; Cystic Fibrosis (CF) represents the most common predisposing factor.Aims and objectivesOur aim is to evaluate clinical and endoscopic findings predictive for sinus mucoceles in pediatric CF population and discuss our surgical management.Methods882 CF patients were followed from 2000 to 2012. During the ENT assessment, complete patient’s history concerning upper airway diseases (nasal obstruction, hyposmia/anosmia, rhinorrhea, snoring) was retraced.Rhinofibroscopical signs suggestive for mucoceles (i.e. obstruction of nasal fossae due to medialization of the lateral wall), were determinant for the execution of CT. Endoscopic sinus surgery (ESS) was performed in case of persistent nasal obstruction and radiological evidence of mucoceles and bones resorption.Results38 children suffered from paranasal sinus mucoceles (mean age 8.3±3.9 years). The most common sites were the anterior ethmoid (55.2%) and the maxillary sinus (44.7%); 7 cases (18.4%) reported bilateral involvement of maxillary sinus ("hourglass image").All patients underwent ESS with the goal of marsupialization of the mucoceles. No complications and recurrences were registered.Clinical improvements and reduction in the use of antibiotics (from 2.92±1,15 to 0.86±0,7 times per year) were achieved in all patients.ConclusionsPrecocious treatment of paranasal sinus mucoceles is essential to prevent complications related to their potential expansion and to eliminate the reservoir of pathogens causing infections of the entire respiratory tract. ER -