TY - JOUR T1 - Congenital pulmonary airway malformation in a 10 year old male adolescent JF - European Respiratory Journal JO - Eur Respir J VL - 38 IS - Suppl 55 SP - p2433 AU - Maria NiƱa Banque Y1 - 2011/09/01 UR - http://erj.ersjournals.com/content/38/Suppl_55/p2433.abstract N2 - Congenital pulmonary airway malformation (CPAM), more commonly and previously termed congenital cystic adenomatoid malformation is an uncommon anomaly characterized by multicystic lesions due to proliferation of the respiratory bronchioles. This lung anomaly has an incidence of 1:25,000-35,000 and 90% of this number occurs in children below 2 years old. Late-onset CPAM is an infrequent illness and requires a high level of suspicion. It usually presents in the form of repeated infections but very rarely remains to be asymptomatic until its diagnosis. This is a case of a previously healthy, apparently asymptomatic 10 year old male adolescent who had an incidental finding of a pulmonary bulla on chest radiograph taken while he was worked up because of a high grade fever which eventually he was diagnosed of dengue fever. He underwent elective right upper lobe lobectomy and was discharged improved on the 4th post-operative day. The final histopathologic result is consistent with a congenital pulmonary airway malformation, type 1. ER -