ILD of known causes | 952 (36.4) | 387 (40.7) | 656 (59.3) | 61.1±12.5 |
CTD-ILD | 631 (24.1) | 198 (31.4) | 433 (68.6) | 60.9±12.2 |
Primary Sjogren's syndrome | 294 (11.2) | 74 (25.2) | 220 (74.8) | 60.9±11.9 |
Rheumatoid arthritis | 121 (4.6) | 56 (46.3) | 65 (53.7) | 67.1±10.4 |
Polymyositis/dermatomyositis | 46 (1.8) | 16 (34.8) | 30 (65.2) | 52.4±12.3 |
Systemic sclerosis | 18 (0.7) | 1 (5.6) | 17 (94.4) | 55.7±11.8 |
Systemic lupus erythematous | 6 (0.2) | 0 (0) | 6 (100) | 56.0 (54.8–64.5) |
Ankylosing spondylitis | 1 (0) | 1 (100) | 0 (0) | 61 |
Mixed CTD | 19 (0.7) | 4 (21.1) | 15 (78.9) | 59.1±11.1 |
Undifferentiated CTD | 126 (4.8) | 46 (36.5) | 80 (63.5) | 58.9±12.4 |
Vasculitis | 161 (6.2) | 79 (49.1) | 82 (50.9) | 65.0 (54.5–72.0) |
Pneumoconiosis | 58 (2.2) | 55 (94.8) | 3 (5.2) | 58.1±12.8 |
Asbestos lung | 23 (0.9) | 9 (39.1) | 14 (60.9) | 63.4±9.1 |
Drug-induced ILD | 28 (1.1) | 17 (60.7) | 11 (39.3) | 63.0±12.3 |
Radiation pneumonia | 21 (0.8) | 13 (61.9) | 8 (38.1) | 64.8±9.8 |
Gastro-oesophageal reflux | 18 (0.7) | 11 (61.1) | 7 (38.9) | 64.3±12.7 |
Others+ | 12 (0.5) | 5 (41.7) | 7 (58.3) | 57.3±15.4 |
Idiopathic interstitial pneumonia | 1367 (52.3) | 898 (65.7) | 469 (34.3) | 64.0 (55.0–72.0) |
Idiopathic pulmonary fibrosis | 692 (26.5) | 551 (79.6) | 141 (20.4) | 65.0 (58.0–72.0) |
Cryptogenic organising pneumonia | 230 (8.8) | 107 (46.5) | 123 (53.5) | 57.3±13.6 |
Nonspecific interstitial pneumonia | 55 (2.1) | 19 (34.5) | 36 (65.5) | 56.8±10.7 |
Respiratory bronchiolitis-associated ILD | 30 (1.1) | 24 (80.0) | 6 (20.0) | 61.4±11.1 |
Acute interstitial pneumonia | 10 (0.4) | 6 (60.0) | 4 (40.0) | 57.0±12.0 |
Lymphoid interstitial pneumonia | 4 (0.2) | 0 (0) | 4 (100) | 67.5 (54.3–74.0) |
Desquamative interstitial pneumonia | 2 (0.1) | 0 (0) | 2 (100) | 55.0 (34.5–58.0) |
Unclassifiable idiopathic interstitial pneumonia | 344 (13.2) | 191 (55.5) | 153 (44.5) | 66.0 (55.0–74.0) |
Granulomatous | 209 (8.0) | 82 (39.2) | 127 (60.8) | 53.5±11.1 |
Sarcoidosis | 147 (5.6) | 54 (36.7) | 93 (63.3) | 53.1±10.4 |
Hypersensitivity pneumonitis | 62 (2.4) | 28 (45.2) | 34 (54.8) | 54.5±12.8 |
Miscellaneous | 87 (3.3) | 53 (60.9) | 34 (39.1) | 44.0±15.9 |
Total | 2615 (100) | 1420 (54.3) | 1195 (45.7) | 62.0 (53.0–71.0) |