Subjects n | 869 |
Males | 320 (36.8) |
Females | 545 (62.7) |
Missing | 4 (0.5) |
Age yrs | 56.6±15.4 (17.0–90.0) |
Time since diagnosis yrs | 1.9±1.8 (0.0–8.0) |
Diagnosis | |
Idiopathic PAH | 160 (18.4) |
Chronic thromboembolic PH | 314 (36.1) |
PH associated with left heart diseases | 59 (6.8) |
PAH associated with connective tissue disease | 200 (23.0) |
Other# | 136 (15.7) |
NYHA class¶ | |
I | 35 (4.5) |
II | 201 (26.0) |
III | 472 (61.1) |
IV | 64 (8.3) |
Primary treatment+ | |
Bosentan | 351 (58.6) |
Sildenafil | 61 (10.2) |
Pulmonary endarterectomy | 102 (17.0) |
Subcutaneous treprostinil | 6 (1.0) |
Epoprostenol/intravenous iloprost | 34 (5.7) |
Inhaled iloprost | 39 (6.5) |
Other | 6 (1.0) |
More than one treatment | 86 (9.9) |