| SSc | Control | p-value |
Subjects n | 58 | 19 | |
Age yrs | 53.5 (45–60) | 42.7 (28.1–50.4) | 0.01 |
Smoker n | 10 | 0 | |
Duration of disease yrs | 5.5 (3.0–10.4) | | |
Modified Rodnan skin score | 8 (4–13) | | |
J′aw,NO nL·min−1 | 6.3 (−9.8–31.3) | 35.5 (25.8–54.9) | <0, 001 |
CA,NO ppb | 6.2 (3.8–9.9) | 2.0 (1.2–3.0) | <0.001 |
R2 | 0.95 (0.92–0.98) | 0.96 (0.95–0.98) | ns |
FeNO50 ppb | 10.1 (5.9–17.8) | 13.1 (11.6–19.6) | ns |
TLC % pred | 92 (77–105) | | |
FVC % pred | 90 (75–104) | | |
FEV1 % pred | 88 (74–101) | | |
Pa,O2 mmHg | 85 (80–98) | | |
DL,CO % pred | 61 (46–71) | | |
DL,CO/AV % pred | 74 (64–85) | | |
sPAP mmHg | 31 (26–36) | | |
sPAP ≥40 mmHg | 8 | | |